ʻO ka maʻi diabetes Phropate i nā keiki > Hoʻopiʻi nā maʻi maʻi

Hōʻike nā hōʻailona mua o ka maʻi phosphate i ka makahiki mua a ʻelua paha o ke ola, ke hoʻomaka ke hele nā keiki (i kekahi manawa ma mua):

i ke ʻano maʻamau o ke keiki
ulu ʻaila
Koi ʻole o nā wāwae,
deformation o ke kuli, a me nā wāwae kuʻekuʻe,
ka laulā o ka iwi ma ka wahi o ka paʻa lima,
hōʻemi i ka kani mele
i ka wā e ʻeha ai i ka kua a me nā iwi (ma kekahi manawa ma muli o ka ʻeha nui, ʻoki ke keiki i ka hele).

ʻO kēia maʻi ka hopena o kahi mutation i ka chromosome X, ke hoʻopau nei i ka hoʻopio ʻana o nā phosphates i nā tubula renal, a laila hoʻihoʻi mai i kahi mana o nā kaʻina pathological e hoʻopili nei i nā kinipona maʻamau o ka calcium ma nā iwi iwi.
ʻO nā kāne e halihali ana i ke aʻa maikaʻiʻole i hāʻawi i kā lākou mau kaikamahine.
Ke hoʻouna nei ka wahine i lawe ʻia i ka lua i nā maʻi i nā keiki o nā kāne a me nā kāne a me nā kaikamahine.

Hoʻomaopopo ʻo LookMedBook: ʻo ka manawa koke i ka huli ʻana i kahi loea no ke kōkua, ʻoi aku ka nui o ka manawa e mālama i ke olakino a hōʻemi i ka hopena o nā hoʻopiʻi:

E kōkua ka lāʻau lapaʻau lāʻau i ka mālama ʻana o nā maʻi

Nā huapau

ʻO ka nānāʻana i ka mōʻaukala olakino a me nā hoʻopiʻi o ka maʻi (ka noiʻi makua):
- ulu ʻala i kahi keiki,
- Koi ʻole o nā wāwae,
- hiki nā hui like, etc.
Hoʻokomo-X-ray o nā iwi (kahi ʻike o nā loli i ka ʻoihana o nā iwi iwi a me nā pilikia ma nā wahi o ka ulu iwi (metaphyses iwi).
ʻO ka nānāʻana i ka urine no nā phosphates (pūhui phosphorus): ke ʻano o ka hoʻonui ʻana i ka nui o nā phosphates (4-5 mau manawa).
Hōʻike koko (hoʻoholo i ka hoʻoneʻe ʻana o ka posforoma ma ke koko i kahi pae o ka calcium).
Ka nānā ʻana genetic e ʻike i nā loli i ka chromosome X i ke keiki.
ʻO kahi kūkākūkā endocrinologist kekahi mea hiki pū.

Hoʻomaʻamaʻa i ka maʻi phropate

Ke koho nei i nā kaumaha he nui o ka vitamina D (i kekahi manawa no ke ola).
Manaʻo, kalumo, nā huaora A a me E.
Ma kahi o nā nāwaliwali o ka palupalu (a i ʻole nā palena) o ke ʻālaʻi, ua hoʻākāka ʻia ka mālama orthopedic (no ka laʻana, ka hoʻoponopono ʻana i ka curvature o ka mākeke me ka hoʻohana ʻana i nā corsets orthopedic kūikawā).
Pono pono ka hoʻomaʻamaʻa ʻana me ka deformations koʻikoʻi o ka pāpaʻi. Mālama ʻia ma hope o ka pau o ka manawa ulu.

Nā hopena a me nā hopena

ʻO ka hōʻino ʻana i ka posture a me ka hoʻololi ʻana o ka ʻūhā ma hope o ka maʻi diabetes phosphate i mālama ʻia i ke wā kamaliʻi e mālama ʻia no ke ola.
Loaʻa ke keiki i ka noʻonoʻo ʻana a me ke kūkulu kino ʻana.
ʻO ka holomua o ka iwi a me ka de artities i ka ʻike ʻole o ka hana kūpono e hiki ke alakaʻi i ka pilikia.
Haki i ka ulu ʻana o nā niho (ke alapine o ke ʻano o ka enamel, ka hoʻonāukiuki ʻana o ka manawa a me ka papa o ka mea, me nā mea āpau).
Ma muli o ka nalowale ʻana (me ka hopena o ka hoʻomōhala ʻana mai o ka ossicles auditory o ka pepeiao waena.
Hiki i ka hopena o ka maʻi ke nephrocalcinosis (ka waiho ʻia ʻana o nā paʻakai kaleka ma loko o nā pūpū), a ma ke ʻano e hiki ke hele i ka hemahema.
ʻO kahi maʻi i loaʻa i ke kaikamahine i ka wā kamaliʻi e hiki ke hana i ka deformity o ka iwi pelvic, ma muli o kahi hana paʻakikī paha ka hana ʻana. Ma ka hoʻomaka ʻana o ka hoʻolālā hāpai ʻana, pono i nā wahine i loaʻa i ka maʻi diabetes phosphate i ka wā kamaliʻi e kūkākūkā me ka mea loea e pili ana i ka ʻāpana cesarean.

Kākoʻo o ka Phosphate Diabetes

ʻO ka ʻike mua i ka maʻi. (Ka manawa kuhikuhi i ka poʻe loea ma ka hōʻailona mua o kahi maʻi no ke kumu o ke ʻano mua a me ke koho ʻana i ka mālama manawa kūpono: ʻo ke kumu nui o kēia mau hana he hoʻemi i nā hōʻeha a me nā hopena hopena).
ʻO ka mālama pono ʻana a me ka mālama mau ʻana i nā keiki me kahi ʻano like like e ka pediatrician a me ka endocrinologist.
ʻO ke kauka ʻana a me nā ʻōiwi olakino no nā ʻohana me ka maʻi diabetes phosphate (kahi i loaʻa ai kekahi o nā ʻohana i kēia ala ma ka wā kamaliʻi) i ke ʻano o ka hoʻolālā ʻana o ka hapai. ʻO ke kumu o kēia hanana ka mea e wehewehe i nā mākua i ka hiki ke loaʻa o kahi keiki maʻi a hoʻomaopopo i ka pili ʻana i nā pōpilikia, nā hopena, nā hopena o kēia maʻi o ke keiki.

Kālai koho

Ua ʻike ʻia kekahi o nā mea nui o ka paepae o ka iwi iwi ka calcium. ʻO ke kumu o ka pīpī o ka iwi me ka kalula ʻo ia hoʻi ka fosfor. Pau ke kanaka i kēia mau mea me ka meaʻai.
ʻO kahi hapa nui o nā phosphates (nā pūhui fosfor) i loko o ke kino kekahi o nā kūlana e pono ai no ka hoʻopili ʻana i ka kalala e nā iwi iwi.
Ma muli o kahi loli ʻana o kekahi o nā huaʻehā chromosome X, ke kīnā ʻole ʻia ka phosphate i nā ʻāpana renal, a ma hope aku ke kaulahao o nā kaʻina pili me nā mea pili i ke kū ʻole ʻana o ka calcium ma nā iwi iwi.

Kūpono ma ka biochemistry o KSMA, 2004
Volkov M.V. Dedova V.D. ʻO nā keiki Orthopedics-Kaukaʻaka, 1980

ʻO ka maʻi diabetes Phropate: nā kumu, nā hōʻailona, nā maʻi, nā mālama

I kēia ao, aneane nā mākua āpau e ʻike i kahi maʻi e like me ka rickets. ʻO nā mea pediatrician āpau mai nā mahina mua o ke ola o kahi pēpē e lūlū i ka pono e pale i kēia ʻano kuʻuna. ʻO nā Rickets e pili ana i nā maʻi i loaʻa ma muli o ka nele o ka cholecalciferol, he mea e ʻike ʻia o ka vitamin D.

Eia nō naʻe, i kekahi mau hihia, ʻike ka ʻōpio o nā keiki i nā hōʻailona o ka patology, ʻoiai ka nānā ʻana o nā hana pale. I kēlā mau hihia, pono e lālū ʻia kahi maʻi e like me ka maʻi phosphate. ʻAʻole e like me rickets, aia kēia maʻi ma nā pathology genetic. No laila, he maʻi koʻikoʻi loa ia a koi aku i ka mālama mau loa.

He aha ka maʻi diabetes?

ʻO kēia ka inoa o kahi hui o nā maʻi āpau e pili ana i ka minerism mineral impaired. Ma kahi ala'ē aʻe, ua kapa ʻia ke pathology me nā huaʻō kūkioki-D-rickets. Ke loaʻa nei ka ʻano nui o ka maʻi diabetes phosphate ma kahi o 1 mai 20,000 mau pēpē hānau hou. ʻO ka maʻi mua ua wehewehe mua ʻia ma ka 1937. Ma hope mai ua hoʻohuli ʻia nā ʻano ʻano ʻē aʻe o ka pathology. ʻO ka maʻi diabetes ka puna ma ka wā ʻōpio. Hoʻowalewale ʻia ka nānā ʻana o nā mākua e ka gait impaired a paʻa i nā iwi.

I nā makahiki he nui, ua aʻo wau i ka pilikia o DIABETES. He makaʻu ke ʻike i ka nui o nā kānaka e make ana, a ʻoi aku ka ulu ma muli o ka maʻi maʻi.

Ua wikiwiki wau e haʻi i ka nūhou - ua hana ka Endocrinological Research Center o ka Russian Academy of Medical Sciences i ka hoʻomohala ʻana i kahi lāʻau lapaʻau e hoʻōla pono i ka maʻi maʻi. I kēia manawa, ke hoʻokokoke nei ka hopena o kēia lāʻau lapaʻau i ka 100%.

ʻO kekahi nūhou maikaʻi: ua mālama ka Ministry of Health i ka hoʻopaʻa ʻana i kahi papahana kūikawā e uku ana i ka uku holoʻokoʻa o ka lāʻau lapaʻau. Ma Lūkia a me nā ʻāina CIS maʻi ma kahi maʻi maʻi mamua hiki i kahi hopena - HE MAU KOA!

ʻO kekahi mau ʻano o nā patologi ke hele pū me nā maʻi metabolic ʻē aʻe. I kekahi manawa he asymptomatic maʻi, a hiki ke ʻike ʻia e nā hoʻokolohua hoʻoliʻi. Hoʻokaʻawale ʻia ka maʻi me nā rickets i loaʻa, ka hypoparathyroidism a me nā ala āpau endocrine. Pono ka hānai ʻana mai ka wā ʻōpio.

Nā kumu kumu o ka maʻi

ʻO ke kumu nui no ka hoʻomohala ʻana i ka maʻi phosphate he mau hana hōʻeuʻeu i ka ʻano genetic. Ua hoʻoilina ʻia nā Mutations. Hiki i nā ʻūlani o nā gen pathological ke lilo i wahine a me nā kāne. Hōʻike ka mutation i ka chomosome X-pili, kahi mea nui. I nā pilikia liʻiliʻi, hiki ke loaʻa ka maʻi diabetes phosphate. Hoʻoulu ia e kū'ē i kahiʻano o nā hina o ka kiko mesenchymal, ka mea i kūkulu ai i ka manawa prenatal. I kēia hihia, ua kapa ʻia ke alahele "he forcogenic rickets."

Aia ka maʻi i ka hui o tubulopathies - hana i ʻole ke āpau. Ma muli o ka hiki ʻana o ka reabsorption o nā minima i loko o ka tubula proximal, ua ulu ka hala o ka phosphorus i ke kino. Eia kekahi, ua kīpī ka hemahema o ka ʻōpū. A ke hopena, ʻike ʻia nā loli o ka hana o ka mineral mineral o ka iwi o ka iwi. ʻO ka pinepine he halaʻole i ka hana o osteoblasts. Huli wale nā kāne i ke ʻano pathologically i kā lākou mau kaikamāhine, a me nā wāhine - i nā keiki o nā kāne like ʻole. E like me ke kānāwai, ʻoi aku ka nui o ka maʻi o ka maʻi ma mua o nā kaikamahine.

Pilikū o Phabetate Diabetes i nā Keiki

Nui kekahi ʻano like o ka maʻi i ʻokoʻa i ka genetic a me nā tapa kulekele. ʻO ka hapa pinepine, ua ʻike ʻia nā kani umauma X-pilina e loaʻa ana i kahi ʻano hoʻoilina. Eia nō naʻe, aia kahi ʻano ʻē aʻe o ka pathology. Penei ka papa o nā ʻano like ʻole o ka maʻi.

E makaʻala

Wahi a WHO, i kēlā me kēia makahiki ma ka honua he 2 miliona mau kānaka e make ana mai ka maʻi diabetes a me kāna mau pilikia. Ke waiho ʻole i ke kākoʻo kūpono no ke kino, e alakaʻi ka maʻi diabetes i nā ʻano kīwī like ʻole, me ka hoʻopau wale ʻana i ka kino o ke kanaka.

ʻO nā hopenaʻoi loa ka mea maʻamau: gangrene diabetes, nephropathy, retinopathy, ʻōpio trophic, hypoglycemia, ketoacidosis. Hiki i nā maʻi kuʻuna ke alakaʻi i ke ulu ʻana o nā maʻi ʻopa maʻi. I ka aneane maʻamau, make kekahi maʻi diabetes, e ʻeha ana me kahi maʻi ʻeha, a huli a lilo i kanaka maoli me kahi maʻi kīnā.

He aha ka hana a nā poʻe me ka maʻi maʻi? Ua kūleʻa ka ʻoihana Endocrinological Research Center o ka Russian Academy of Medical Sciences i ka hana ʻana i ka hoʻoponopono e hoʻōla pono i ka maʻi mellitus.

Ke hana nei ka papahana Federal "Pūnaewele Haumaha", i loko o ka papa o kēia lāʻau lapaʻau i hāʻawi ʻia i nā mea noho a pau o ka Lūkini Lūkini a me ka CIS - LAHUI . ^ E Ha yM. No ka ʻike hou aku, ʻike ka pūnaewele mana o MINZDRAVA.

X-pili kikina ʻano nui o ka maʻi phosphate. Hōʻano ʻia ia e nā loli a ka huahelu PHEX, nāna e hoʻopuni nā endopeptidase. Hāpai kēia enzyme no ka lawe ʻana i nā minima like ʻole ma o nā kahiki wai o nā pūpū a me nā ʻāpana liʻiliʻi. Ma muli o ka genation gen, ke hoʻomoe nei kēia kaʻina hana, kahi e hoʻolilo ai i kahi hemahema o nā iʻa phosphate i loko o ke kino.
Xeneleu pilina pili X-pili. Hoʻohālikelike ia me ka hoʻohālikelike ʻana o ka hua CLCN5, ka mea e kāpae i kahi protein e kuleana ai no nā hana o nā kaila wai klorida. Ma muli o ke kuhihewa, ka hoʻopau ʻia ʻana o nā mea āpau ma o ka membrane o nā ʻāpana renal i hoʻopau ʻia. Hiki i nā mea lawe i kēia ʻano papaʻaina ka wahine a me ke kāne. Eia naʻe, hoʻomake ka maʻi i nā keiki kāne.
ʻO Autosomal ka mana nui o ka maʻi phosphate. Hoʻohui ʻia me ka genation mutation ma chromosome 12. Ma muli o ke kīnā ʻole, hūnā ka osteoblasts i kahi protein pathological e hoʻoikaika ana i ka hoʻonui ʻia ʻana o nā phosphates mai ke kino. Hōʻike ʻia ka pathology me kahi papa maʻalahi, me ka hoʻohālikelike ʻia me nā palapala pili X.
Ka ʻano ʻōiwi Autosomal. Heʻilihue kaʻai. Hōʻike ʻia ia e kahi hemahema i ka lā DMP1 i loaʻa ma ka chromosome 4. Hoʻopili i ka protein i kuleana no ka hoʻomohala ʻana o nā iwi a me nā dentin.
Ka maʻi hoihoi autosomal, i hele pū me ka excretion o kalima i ka pā. Hōʻike ʻia ia ma muli o kahi kuhi i kekahi gen ma loko o ke chromosome 9 a me ke kuleana no ka hana ʻana o nā kanaleka kīpē o ka sodium.

Ma kahi o nā papa inoa inoa inoa o ka diabetes Phate, aia kekahi mau ʻano o ka pathology. ʻO nā ʻano like o nā maʻi i aʻo ʻole ʻia.

Nā ʻokoʻa ma waena o ka Rickets a me ka Phosphate Diabetes

ʻAʻole pololei nā mea like ʻole ʻo ka rickets a me ka phosphate i nā keiki. ʻO nā ʻokoʻa ma waena o kēia mau papa i ka etiology a me ke ʻano o ka hoʻolālā ʻana. ʻO nā rickets maʻamau ka loaʻa i kahi maʻi i pili me ka nele o ka cholecalciferol. Kuhi ʻia kēia mea i loko o ka ʻili ma lalo o ka mana o ka lā. He mea maʻamau ia i ka hopena maʻi ma kahi o ka waiola D i kēlā me kēia lā no nā keiki mai 1 mahina a hiki i 3 mau makahiki he nui, ʻaʻole ka manawa o ke kauwela. Ma muli o ka nele o ka cholecalciferol, ke hoʻopau nei ke kaʻina o ka hoʻopili ʻana o ka calcium. ʻO ka hopena, ulu ka ulu ʻana o ka iwi.

ʻO ka ʻokoʻa ma waena o ka maʻi phosphate, ʻo ia nō e pili ana i nā maʻi congenital. Me kēia patula, ʻike ka hoʻopiʻi ʻana o nā minela i loko o nā keiki, ma nā ʻano phosphates. I kekahi mau hihia, ua hoʻomaopopo ʻia ka hemahema o ka calcium. Ma muli o ka halaʻole o ka mineralula o ka kiko o ka iwi, ua like nā hōʻailona o nā ala. Hiki ke hoʻokumu ʻia ka ʻokoʻa ma waena o lākou ma hope o nā diagnostics laboratorium.

ʻO nā maʻi he hypophosphatemic i loko o nā pēpē: hōʻailona o ka maʻi

Hoʻomaopopo ka hōʻailona o nā maʻi i ka makahiki ʻelua o ke ola. I nā hihia pilikia, ʻike ʻia nā rickets hypophosphatemic i nā pēpē. ʻO nā ʻōpuhi e hiki ke hōʻike i ka wā kamaliʻi, ʻo ia ka hypotension a me ke pōkole o ka wāwae. ʻO nā hōʻike hōʻike pilikino nui ka:

ʻO ka hoʻonālikelike o nā hana o nā wāwae.
ʻO ka curvature o O o nā o nā haʻahaʻa haʻahaʻa.
Ke kuʻi nei ka ulu ʻana i nā keiki - e nānā ʻia ma hope o 1 makahiki.
Hoʻoweliweli ana i nā wīwī a me nā kāwili kūloko - "rickety bracelets a me ka rosary."
ʻO ka ʻeha ma nā iwi pelvic a me nā spine.
Hōʻino i ka enamel niho.

ʻO ka pinepine loa, ʻo ka hoʻopiʻi nui a nā mākua he ua hāmeʻe nā wāwae i ka pēpē. Ke holo nei ka maʻi, puka mai ka palupalu o ka iwi - osteomalacia.

ʻO kā mākou mea heluhelu e kākau nei

I ka 47, ua hōʻike wau i ka maʻi diabetes 2. I kekahi mau pule ua loaʻa iaʻu kahi aneʻi 15 kg. ʻO ka luhi mau, ke hiamoe nei, ke ʻano nei i ka nāwaliwali, ʻike ʻia ka ʻike e noho.

I kaʻu ʻana i 55, ua ʻake wau iā wau iho me ka insulin, mea ʻino loa nā mea a pau. Hoʻomau ka maʻi e hoʻomaka ana, hoʻomaka ka hopu kino, ua hoʻihoʻi maoli wau i ka ambulance mai ka honua aʻe. I nā manawa a pau aʻu i manaʻo ai ʻo kēia ka manawa hope loa.

Ua hoʻololi nā mea a pau i ka wā a kaʻu kaikamahine e heluhelu iaʻu i kahi ʻatikala ma ka Pūnaewele. ʻAʻole hiki iā ʻoe ke noʻonoʻo i koʻu aloha iā ia. Ua kōkua kēia ʻatikala iaʻu e haʻalele loa i ka maʻi diabetes, kahi maʻi maʻi i hoʻopuni ʻia ʻole. ʻO nā makahiki 2 i hala ua hoʻomaka wau e neʻe hou aku, i ka pūnāwai a me ke kauwela aʻu e hele ai i ka'āina i kēlā me kēia lā, alakaʻi mākou i kahi ʻano hana me kaʻu kāne, huakaʻi hele. Hōhā ka poʻe a pau i ka hoʻomau ʻana wau i nā mea āpau, kahi e nui ai ka ikaika a me ka ikaika. ʻAʻole lākou e manaʻoʻiʻo i koʻu makahiki he 66.

ʻO wai e makemake e ola i kahi ola lōʻihi, hoʻopoina a poina i kēia maʻi weliweli loa, e lawe i nā minuke 5 a heluhelu i kēia ʻatikala.

Ka hoʻomaikaʻi ʻana i nā rickets a me ka maʻi diabetes

Hoʻohana ʻia nā nui o nā cholecalciferol e mālama i ka maʻi diabetes phosphate. I kekahi mau hihia, ua hōʻike ʻia ka hoʻomākaukau ʻana o ka calcium. E noʻonoʻo e hoʻohana i nā lāʻau lapaʻau e pili ana i ka phosphorus. No ka hoʻomaikaʻiʻana i ke kūlana, ua kuhikuhi ʻia nā meaʻala a me nā mineral. Hoʻopili kēia me ka hoʻomākaukau ʻana "Vitrum", "Duovit", "Alphabet", etc.

Me ka curvature koʻikoʻi o nā iwi, hōʻike ka hoʻomaʻamaʻa ʻana i ke kino. Kūkākūkā ʻia me kahi mea lapaʻau orthopedic.

Moʻolelo o kā mākou poʻe heluhelu

Puhi ka maʻi maʻi ma ka home. Ma kahi mahina aʻe ua poina iaʻu e pili ana i nā poho i ka kōkō a me ka lawe ʻana i ka insulin. Auē, pehea wau i pilikia ai, nāwaliwali mau ʻana, ke kāhea mai nei i ka pilikia. ʻEhia mau manawa i hele aku ai i ka endocrinologists, akā haʻi wale lākou i ka mea hoʻokahi - "Lawe i ka insulin." A i kēia manawa 5 mau hala, e like me ka maʻamau o ke kō o ke koko, ʻaʻole hoʻokahi iki manawa o ka insulin a hoʻomaikaʻi nui loa i kēia ʻatikala. Pono nā kānaka āpau me ka maʻi maʻi!

Nā hana kūpono a me ka prognosis

Hoʻokomo ʻia nā hana pale i ka hoʻokolohua o ka pediatrician a me nā mea hoʻokipa, hele i ka lewa hou, ke koho ʻia o ka vitamin D mai ka mua o ka malama o ke ola. Inā aia nā mea maʻi me ka diabetes phosphate i loko o ka ʻohana, pono kahi hana genetic i ka wā o ka hoʻomohala ʻana i ka maʻi fetal. Hoʻonui maikaʻi loa ka prognosis me ka mālama manawa.

ʻAʻole hewa paha nā poʻe like ʻole e nānā i nā kiʻiʻoniʻoni. Eia nō naʻe, i loko o nā kiʻiʻoniʻoni maikaʻi loa aia nā hewa a nā mea e ʻike e nānā.

Mai hana i kēia mea i ka hale pule! Inā ʻaʻole ʻoe maopopo e pili ana paha i ka pololei ʻana o ka hana ma ka hale pule, a ʻaʻole paha, a laila paha ʻoe e hana ana i ka hewa.Eia kahi papa inoa o nā mea weliweli.

Pehea e nānā ai i nā ʻōpiopio: ʻo nā pākiki maikaʻi loa no ka poʻe ma luna o 30, 40, 50, 60 mau kaikamahine i loko o 20 mau makahiki ʻaʻole e hopohopo i ka ʻano a me ka lōʻihi o ke kaila. ʻIke ʻia ua hana ʻia nā ʻōpio no nā hoʻokolohua i ka helehelena a me nā puʻupuʻu wiwo ʻole. Akā, ʻo ka mea hope loa.

9 He mau wahine kaulana i hāʻule i ke aloha me ka wahine. ʻAʻole hiki iā ʻoe ke kāhāhā a kāhāhā paha i kekahi ke haʻi ʻoe iā ia.

No ke aha mākou e pono ai i kahi ʻōpala kūpeʻe liʻiliʻi? ʻIke ka poʻe āpau he pāloko iki ma luna o nā jeans, akā he liʻiliʻi kekahi i manaʻo e pili ana i ke kumu e pono ai. ʻO ka mahalo loa, ʻo kahi mea no ia hr.

ʻAʻole hiamoe o ko mākou kūpuna e like me mākou. He aha ka mea hana hewa ʻole mākou? He paʻakikī hiki ke manaʻoʻiʻo, akā he nui nā kumu ʻepekema a me nā mea kākau moʻolelo i manaʻoʻiʻo ʻole ka hiamoe o kēia kanaka e like me kona mau kūpuna kahiko. Ke kumu kumu

ʻO ka maʻi diabetes Phropate: hana, hōʻailona, nā keiki

ʻOiai ke kau nei o ka inoa o kēia maʻi me ka huaʻōlelo a ka maʻi diabetes, ʻaʻohe pili o ka hana o ka pancreas, nā pilikia me ka insulin a me ka glucose o ke koko. Eia naʻe, makemake kā ka diabetes diabetes iā mākou wale nō ma muli o kona inoa, akā no ka mea nō ia e hoʻomohala ma muli o ka hōʻino o ka metabolic, a ʻo ia kekahi o nā kumuhana ma kā mākou pūnaewele.

ʻAʻole ʻike ka poʻe a pau, ma ka lāʻau lapaʻau, hiki ke kāhea ʻia ʻo ka maʻi diabetes not the only mellitus o ke ʻano mua a ʻelua paha. Hoʻomaopopo ʻia nā maʻi Diabetes, he hui āpau o nā maʻi me nā kumu like ʻole, akā me nā hōʻailona like:

makewai nui loa
hookeau pinepine,
kahi loli koʻikoʻi i ka haku ʻia o ka urine.

ʻO ka maʻi diabetes Phropate ka like me nā maʻi ʻē aʻe o kēia pūʻulu, ʻaʻole wale ka maʻi, akā, ka pale ʻana hoʻi i nā kaʻina metabolic i loko o ke kino. Eia nō naʻe, aia kahi ʻokoʻa nui mai ka maʻi maʻi - kahi genis predisposition. I nā huaʻōlelo ʻē aʻe, ua hoʻoili ʻia ka diabetes phosphate a maʻalahi ke pale i kona kū a me ka hoʻomohala ʻana ma kekahi ʻano.

Hoʻouna ʻia ka maʻi mai nā kāne wale nō i nā kaikamahine i 100 ka nui o nā hihia. ʻO ka mea lawe i ka maʻi phosphate hiki ke lilo i makuahine, nāna e hoʻoiho i ka maʻi i kāna mau kaikamahine a me nā keiki kāne like.

Aia kekahi mau lāʻau lapaʻau e ʻōlelo ana ua ʻoi aku ka hopena o ke kāne male i nā hōʻailona o ka maʻi ma mua o ka wahine. I nā hihia ākea ka hopena, e ʻike ʻia nā neoplasms o nā palupalu palupalu a me nā iwi, akā, ʻo ia ka hiʻohiʻona o ka poʻe ʻelemakule.

Nā hiʻohiʻona o ka maʻi

E like me ka mea i hōʻike mua ʻia, ua like like ka suka diabetes phosphate me ka maʻi maʻamau metabolic maʻamau. Aia kekahi maʻi āpau i loaʻa nā hiʻohiʻona maʻamau - ʻo ia kahi o nā ʻano kahakalē. I kēia hihia, ʻike pū ʻia ka ulu ʻana o ka iwi kō ma muli o ka hoʻopalike ʻana o ka puna me ka whakawhitinga o ka phosphorus a me ka calcium.

Hiki i nā maʻi diabetes Phropate i nā keiki me ka nele o ka mauʻu D, a i nā pākeke ka mea i hōʻike ʻia e ka curvature o nā iwi a me kā lākou palupalu. ʻO kekahi inoa ʻē aʻe no ka phosphate diabetes:

Pākuʻi vitamin D-hilinaʻi,
helehelena o ka lua,
familial congenital rickets,
ʻO ka holo wāwae hypophospholenic.

Mālama wale ia, i kēia maʻi aia, he mau hewa i ka lawa o ka hoʻopili ʻana o ka calcium a me ka phosphorus, e pale ana i ka iwi o ka iwi mai ke ʻano maʻamau. Eia kekahi, aia nā pilikia e komo i loko o ke kino o ka vitamina D, pono e hoʻololi i nā mea kūikawā e like me nā hormone.

Hoʻololi ʻia ka maʻi diabetes Phropate i kēlā me ke kue ʻole i ka hana o nā mea pono e pono ai ke kino mai ka vitamin D a i ʻole ka hoʻoweliweli ʻana o nā ʻili i loko o ia mea e hoʻemi wale. ʻO kēlā kalona a pau i kū ʻole ʻia e nā iwi aia pau loa i ka wā o ka urination.

Hoʻohālikelike ka hopena o ka phosphate diabetes i nā maʻi me nā rickets untreated. Ke ulu nei ke keiki, hoʻokaumaha ʻia ke kaʻe o nā iwi o kāna iwi, a ma muli o nā hihia koʻikoʻi a nalowale paha, hiki i ke keiki ke lilo i ka hiki ke neʻe kūʻokoʻa.

Hiki i kahi hui kīnā ke hoʻoweliweli i ka poʻe maʻi ma ka mea kahi e lilo ai ka maʻi i ka maʻi lalo. ʻO ka paleʻana i ka laweʻana o ka calcium i kēia hihia he exacerbated wale nō.

Nā maʻi maʻi

I kahi kūlana maʻamau, hele mai ka hānai o ka phosphorus i nā tubula renal a ke kāohi ʻia i ka vitamin D. ʻO kona hopena e like me ka insulin, me nā glucose e hiki ai i loko o nā pūpū - ma nā ʻano like ʻole o nā huaʻai e kōkua ai i ka hoʻonaninua ʻana i ka phosphorus.

Ma ka maʻi diabetes, ʻaʻole hiki i kēia kaʻina: ʻaʻole hiki i ke kino ke hoʻōla i ka lāʻau a hoʻokaʻawale i nā mea e pono ai o ia, a i ʻole kēia mau mea, akā ʻaʻole nā mea i ʻike ʻia. Ma muli o kēia, ʻaʻole paʻa nā kolo o ka phosphorus i ke kino. Hoʻopilikia pili kēia pili i nā ʻāpana āpau, ʻoi aku ka nui o ka ʻōnaehana musculoskeletal.

ʻO kēia no ka pili pono o ka pilina o ka phosphorus a me ka calcium. Inā ʻaʻole hoʻopili ʻia kēia mau mea ʻelua i ke kino, ʻaʻole hiki i nā iwi a me nā ʻāpana ke loaʻa i ka ikaika e pono ai. No ke aha e hiki ai kēia mea?

Nā kumu kumu o ka maʻi Phosphate

ʻO nā maʻi i hoʻoili ʻia i ka diabetes phosphate e nānā pinepine i ka genetically. Ua helu ʻia kēia mau maʻi hoʻoilina ʻelima hui:

Hoʻokomo ka ʻano mua me nā hihia i ka wā e hoʻopili ʻia ai ka hua "hewa" ma ke X chromosome a he mea lanakila nui. Ke manaʻoʻiʻo ia nei me kēia ʻano o ka haunaele, ka paʻakikī o ka lawe ʻana i nā papa o ka phosphorus i nā cell. Ke lohi nui nei kēia kaʻina hana a hoʻonui koke i ka phosphates i ka urine me ka ʻole e hōʻea i nā iwi iwi. ʻO ka hopena ka pae ʻana o ka wahine i kēia genes e 50% - akā e hāʻawi ʻia ʻo ia i nā keiki o nā kāne like ʻole, aia nā kāne i ka ʻenekena i 100% o nā hihia - akā koe wale nō i nā kaikamahine.
Hoʻopili hou ke ʻano lua, ua pili pū ka lua maikaʻi i ka chromosome X, akā pili wale i nā kāne, wahine hana wale nō e like me nā mea lawe. Hōʻalo kēia ʻano ira i ke ʻoiaʻiʻo o ka hōʻiliʻili o ke koikoi o nā ions a pau i loko o ke kumu, ua wehe ʻole ʻia nā lua.
ʻO ke ala maʻalahi loa o kēia ʻano maʻi maʻi ʻo ia ke kolu o ke ʻano. I ka hopena o nā loli genetic, ua hana ʻia kahi protein e hoʻonui i ka hoʻonui ʻana i nā phosphates ma o nā kanu urinary.
Ma kahi ʻano maʻi maʻi autosomal hiki wale nō inā nānā nā mākua ʻelua i ka lāʻau ʻalapiha. ʻAʻole maopopo i kēia ʻano maʻi maʻi maʻi.
Hoʻololi ʻia ka ʻaoʻao hope o ka maʻi maʻi e ka urries excretion o ka phosphory wale nō, akā ʻo ka calcium. I ka manawa like, ua emi iki kā lākou manaʻo i ke koko.

Loaʻa ʻole nā ʻaoʻao ʻelua hope loa.

I nā hopena ākea nui, hiki i ka maʻi diabetes phosphate ke hoʻomohala i nā pākeke ma muli o ka maʻi pūpū.

Nā hōʻailona o ka maʻi

ʻO nā ʻōlapa Hypophosphatemic, ʻaʻole like me ka maʻamau, ʻaʻole ia i hōʻike koke iā ia iho, akā ma ka 1,5-2 mau makahiki, i ka manawa i hoʻomaka ai ke keiki e hele. Hoʻololi ʻokoʻa loa ke kiʻi olakino o nā maʻi like ʻole o ka phosphate i nā keiki - i kekahi manawa hiki ke hoʻoholo ʻia ma o ka nānā ʻana, i nā kūlana ʻē aʻe, ua ʻike ka helehelena o nā pilikia i like me nā ʻano maʻamau. E ʻike paha nā mākua a me nā kauka i kēia mau hōʻailona:

ka ʻāhā o nā wāwae, ka mea i ʻike i ke kaʻina o ke aʻo ʻana o ke keiki e hele,
stunting, pilikia me ke ʻano o nā niho, palupalu,
hoʻowahāwahā gait, ke lele ana ke keiki mai kēlā ʻaoʻao a i ʻole hiki ʻole ke hele me ka ʻole o ke kākoʻo.
ka iwi ʻōpala, kahi e hele ai i nā pilikia pinepine;
Hoemi ʻia ka hana a ke keiki, ua ʻino ʻo ia i ko lākou hoʻāʻo e hoʻoikaika iā ia i ka hana pilikino,
ka nunui o nā iwi o nā wāwae kokoke i nā ʻāpana.

ʻO kaʻoiaʻiʻo, aia paha a ʻike ʻia paha kekahi o kēia mau maʻi i ke keiki olakino, no laila ʻaʻole i hoʻohilahila koke nā mākua. Akā inā ʻeha ke keiki i ka ʻeha i kēlā me kēia manawa e kau ai iā ia ma mua o kona mau wāwae, he manawa kūpono ia e kamaʻilio i ke kauka a e hoʻomaʻamaʻa.

ʻAʻole paʻakikī ia i kahi loea e hoʻokaʻawale i ka maʻi maʻamau o ka phosphate mai nā rickets maʻamau: me nā loli hōʻeha hope loa, ua loli nā iwi āpau i nā loli, a me nā iwi wale nō a me nā ʻāpana o nā wāwae i loaʻa i ka hypophosphatemic.

ʻO nā ʻōhua hiki

Me ka mālama manawa kūpono, hiki ke hoʻopau ʻia nā hoʻopiʻi. Akā inā ʻaʻole ka hopena o ka hoʻololi ʻana o ke kāʻei a paʻa ʻole i kēia manawa, e mau ana ia no ke ola. ʻO kēia paha ka curvature o nā wāwae a i ʻole pōkole loa. ʻO nā maʻiʻeha i nā iwi pelvic i nā wahine he mau kumu no ka ʻāpana cesarean i ka wā hāpai. ʻO ka hapai, ʻo ka piʻi ʻana o ka hōʻeha i kēia maʻi ma kahi keiki.

Kūkulu, Kākoʻo

Me ka mālama kūpono i ka wā kamaliʻi, hiki i ka maʻi ke hōʻike wale iā ia iho i kēlā me kēia manawa i ka manawa e hoʻonui ai ka manaʻo no ka phosphorus a me ka calcium. Pili kēia i ka wā'ōpiopio, ka wahine hāpai a me ka lactation. I kēia manawa, pono e lawe i nā huaora e pono ai a me nā minela a me ke kahe mau o ke kauka. Pono ʻo ia e nānā i ke kiʻi o nā hoʻokolohua no ka loaʻa ʻole o ka calcium, ka phosphorus a i nā mea vitamina.

ʻO ka poʻe loaʻa ka maʻi genetic nei e noʻonoʻo pono i ka mea i hoʻoili ʻia ka maʻi, a kūkākūkā i kēia me ke ʻano hoʻi o ka hoʻokumu ʻana i kahi ʻohana. Inā loaʻa ka wahine i ka lolo o ka phosphate a lilo i ka wahine, pono ia e ʻōlelo i kāna kauka e pili ana i ka hele mai o kēia maʻi. ʻO ka hōʻemi kēia o nā pilikia no ka makuahine a me ka mālama kūikawā e nānā i ke olakino o ke keiki.

Maikaʻi paha kekahi mea inā he pēpē ka loaʻa ʻana o kahi pēpē me hapa ira kahi 50%, a laila e noʻonoʻo pono ka hapalua lua. ʻAʻole pela kēia, ʻo ka hopena o ka hoʻoili ʻana i ka diabetes phosphate i kahi keiki lua e noho mau loa ma ke kiʻekiʻe kiʻekiʻe.

ʻOiai ke hoʻomau nei ʻo ka maʻi phosphate i kahi maʻi genetic incurable, me ka manawa kūpono e kipa aku ai i ke kauka, ka nānā ʻana i ke kūpono, ka mālama kūpono ʻana a me ka hopena koʻikoʻi no ka lawe ʻana i nā lāʻau lapaʻau ma loko o ke ala āpau, hiki nō ke alakaʻi i kahi ʻano lōʻihi, lohi ʻia.

Pehea ka hana ʻana o ka lolo?

I ke wā kamaliʻi, ʻoi aku ka nui o ka calcium a me ka phosphorus ma mua o nā pākeke. No kēia kumu, ʻoi aku ka paʻakikī o nā hopena o nā maʻi i nā keiki.

ʻO nā hōʻailona kai i ʻike ʻia me ka maʻi diabetes phosphate:

ka mea i kapa ʻia ʻo ka duck,
e ulu ana ka ulu ʻana ma lalo o ka awelika,
ka papahele o nā ʻoi aʻe o lalo, a ma nā wāwae i lalo, me nā leka O,
ke'ōmaʻomaʻi manuahi.

I kona wā ʻōpio nui, hiki ke maʻi ka maʻi diabetes phosphate ma hope o ka hōʻike ʻana o nā mākua i ka hana haʻahaʻa haʻahaʻa o ke keiki. I kekahi mau hihia, hiki i nā pēpē ke uē a walaʻau paha, ʻoiai inā pono ʻoe e hele. ʻO kēia no ka hōʻeha o ka iwi.

Me nā rickets, ua nāweli nā iwi a hiki i ka ʻike ʻole o ka curvature akaka, hiki ke loaʻa i ka maʻi i ka hihia ʻo nā palaka puʻupuʻu i waena o ke keiki.

Aia kahi hiʻohiʻona koʻikoʻi o nā rickets a me nā congenital. Inā hiki ke mālama ʻia ka mea mua i nā mahina mua o ke ola o ke keiki, a laila ma ka lua aia wale nō ma hope o 6 mau mahina a i ʻole 1.5-2 mau makahiki (ma hope o ke hoʻomaka ʻana o ke keiki).

Hiki ke hoʻoponopono pololei ʻia i kēia maʻi me ke kōkua o:

hōʻike koko no ka biochemistry,
x-ray noiʻi.

Nā ʻano biochemistry o ke koko a me nā iwi iwi e ʻokoʻa me nā ʻano ʻano like ʻole. Inā he kānalua i ka lolo o ka phosphate, a laila ma kēia hihia, e hōʻike aku nā kauka i nā makua o ke keiki e hoʻomaʻamaʻa i nā hōʻike kūpono.

Hiki paha i ka hoʻokuʻuʻana i nā mea kahiki congenital?

ʻO ka mea nui o ka nānāʻana o nā rickets papa a me ka diabetes phosphate e like nō. Hoʻopilikia ka mea lapaʻau i ka hoʻokomo ʻana o nā ʻōmole o ka nui o ka vitamina D i loko o ke kino o ka mea maʻi.

I ka wā e mālama ai nā kauka, e nānā pono nā kauka i ka paʻa o ka phosphorus i ke koko, a me kāna mau hiʻohiʻona ʻē aʻe biochemical. Pono kēia no ke koho ʻana o nā ʻōnaehana pono.

Pono e hoʻōla ʻia nā mea kanu huaola me ka hoʻomākaukau ʻana o ka fosfor, a me kahi mea hoʻomohala kūikawā i kūkulu ʻia, kahi mea e pono ai nā meaʻai a ka momona.

ʻAʻole hiki i nā wā maʻamau ke kamaʻilio e pili ana i kahi maʻi maʻi mua. I kekahi mau hihia, hiki i nā kauka ke noi aku e kali a hiki i ke keiki i ka makahiki 3 mau makahiki.

ʻO kekahi manawa liʻiliʻi ka liʻiliʻi o ka lāʻau lapaʻau a me ka pono o nā lāʻau lapaʻau, akā naʻe, ʻaʻole maʻamau mau ke kamaʻilio e pili ana i ka pau pau ʻana o ka maʻi fosfatate.

Ma ka maʻi mellitus o ka ʻano mua, ʻaʻole hiki ke hoʻihoʻi hou i ka hana o kekahi insulin. No laila, ʻo nā pilikia me ka calcium, he paʻakikī ke hoʻokomo.

Inā loaʻa i nā mea maʻi ʻokoʻa ka nui o ka hoʻohana ʻana i ka calcium a me ka phosphorus, no laila i ka wā ʻōpio a me nā wā'ōpiopio ke makemake nui nei i kēia mau mea. Pili ka lula like i ka manawa o ka wā hāpai i ka wahine a me ka lactation.

ʻAʻole hiki ke hoʻoponopono i nā hopena i ka papa o ka maʻi maʻamau. No ke ola, e noho ana ke kanaka:

kūlana ʻoki pōkole
kaheʻe o nā o nā haʻahaʻa haʻahaʻa.

ʻO ia ka hopena hope loa o nā rickets no ka wahine i lilo i mea pono mua no ka haʻalele ʻana i ka hānau keiki maoli a koho i kahi ʻāpana cesarean.

Kākau i nā manaʻo

Inā ʻoe e heluhelu i kēia mau laina, hiki iā ʻoe ke manaʻo e maʻi ʻoe a i aloha paha kāu mea aloha.

Lawe mākou i kahi hana noiʻi, ua noiʻi i kahi pūpū o nā mea ʻona a nui loa ka nānā ʻana i ka hapa nui o nā ala a me nā lāʻau lapaʻau no ka maʻi maʻi. Eia ka ʻōlelo penei:

Inā hāʻawi ʻia aku nā lāʻau āpau, he hopena wale nō ia, ma ka manawa i pau ai ke komo ʻana, ua nui ka maʻi.

ʻO ka lāʻau lapaʻau wale nō i lawe i nā hopena koʻikoʻi he DIAGEN.

I kēia manawa, ʻo kēia wale nō ka lāʻau i hiki ke ho'ōla i ka maʻi diabetes. Ua hōʻike ʻo DIAGEN i kahi hopena ikaika loa i ka hoʻomaka mua o ka maʻi maʻi.

Ua noi mākou i ka Oihana Ola:

A no nā mea heluhelu o kā mākou pūnaewele ke loaʻa i kēia manawa kahi manawa e loaʻa ai iā DIAGEN HE MAU KOA!

Hoʻolohe Ua lilo pinepine nā kumu o ke kūʻai ʻana i DIAGEN hoʻopunipuni.
Ma ka kau ʻana i kahi kauoha e hoʻohana ana i nā loulou ma luna, e hōʻoiaʻiʻo ʻoe e loaʻa ka huahana maikaʻi mai kahi mea hana. Eia kekahi, ʻo ke kūʻai ʻana ma ka pūnaewele mana, loaʻa iā ʻoe ka hōʻoia no ka hoihoi (me ke kumukūʻai o ke kaʻa), inā ʻaʻole i loaʻa ka hopena o ka lāʻau lapaʻau.